Wegener′s granulomatosis presenting as spontaneous pneumothorax in young adult

Spontaneous pneumothorax in Wegener's granulomatosis.

Wegener's granulomatosis is a disease characterised by necrotising granulomatous angiitis of the upper and lower respiratory tracts, a necrotising glomerulonephritis, and a diffuse small vessel vasculitis that may affect almost any organ system.' Various pulmonary lesions have been described, but pneumothorax has seldom been mentioned. We report a patient who developed a spontaneous pneumothora...

Bronchopulmonary sequestration presenting as a spontaneous pneumothorax.

Bronchopulmonary sequestration is a relatively rare medical condition wherein a mass of nonfunctioning primitive lung tissue does not communicate with the tracheobronchial tree and receives its blood supply from an anomalous systemic artery.1-6 It usually manifests at younger ages and is rare in adults. Its clinical presentation varies in adulthood.1-3 We report the case of a young male adult w...

Marfan's syndrome presenting as bilateral spontaneous pneumothorax.

A case of bilateral spontaneous pneumothorax in a 14-year-old girl with previously undiagnosed Marfan's syndrome is described. The pulmonary abnormalities of Marfan's syndrome are not commonly encountered and bilateral pneumothorax is itself a rare event which, in most instances, has been reported following invasive procedures.

ENT manifestations of Wegeners granulomatosis.

Wegeners granulomatosis is a necrotizing granulomatous vasculitis with multisystemic involvement. We present two cases of Wegener's presenting with otological manifestations as the first symptom. These symptoms are subtle and diagnosis may be easily overlooked. Hence a high index of suspicion is required. Early diagnosis and treatment goes a long way in improving the outcomes and in preventing ...

Spontaneous pneumothorax as a presenting pulmonary manifestation of early sarcoidosis.